眼科学报2001，Vol.17Issue(3)：163-167,5.
A Case of Erdheim-Chester Disease with Bilateral Orbital Involvement
A Case of Erdheim-Chester Disease with Bilateral Orbital Involvement
Zhongyao Wu 1Jianhua Yan 1Wende Hong 2Yaoxian Yuan 2Lijun Dai2
作者信息
- 1. Zhongshan Ophthalmic Center, Sun Yat-sen University of Medical Sciences, Guangzhou, 510060 China
- 2. Department of Hemotology, The First Affiliated Clinical College Sun Yat-sen University of Medical Sciences, Guangzhou 510080 , China
- 折叠
摘要
Abstract
Purpose: To describe a case of Erdheim-Chester disease with bilateral orbital involvement.Methods: A 43-year-old female with bilateral proptosis was presented. Its clinical features, image findings, pathological character and therapeutic effect were evaluated.Results: CT demonstrated bilateral, diffuse orbital mass. Histopathologic assessment revealed a diffuse xanthogranulomatous process with clusters of lipidladen histocytes. Numerous Touton giant cells were scattered throughout the lesion. Renal and heart failure happened during a 6-year follow-up period. Long bones roentgenogram demonstrated diffuse symmetrical sclerosis with extensive, lytic lesions. Systemicadministration of corticosteroids, chemotherapy, immunoglobulin and traditional Chinese medicine showed good therapeutic result. Conclusions: An administration of systemic corticosteroids, chemotherapy, immuno- globin and traditional Chinese medicine can control Erdheim-Chester disease. Further exploration of its pathogenesis and collection of useful clinical data are required.关键词
Erdheim-Chester disease/Orbit/TreatmentKey words
Erdheim-Chester disease/Orbit/Treatment分类
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Zhongyao Wu,Jianhua Yan,Wende Hong,Yaoxian Yuan,Lijun Dai..A Case of Erdheim-Chester Disease with Bilateral Orbital Involvement[J].眼科学报,2001,17(3):163-167,5.
