首页|期刊导航|中华医学杂志（英文版）|Clinical features and imaging findings in pulmonary capillary hemangiomatosis: report of two cases and a pooled analysis

Clinical features and imaging findings in pulmonary capillary hemangiomatosis: report of two cases and a pooled analysis

XIE Wan-mu DAI Hua-ping JIN Mu-lan WANG Zhen YANG Yuan-hua ZHAI Zhen-guo WANG Chen

中华医学杂志（英文版）2012，Vol.125Issue(17)：3069-3073,5.

中华医学杂志（英文版）2012，Vol.125Issue(17)：3069-3073,5.DOI:10.3760/cma.j.issn.0366-6999.2012.17.019

Clinical features and imaging findings in pulmonary capillary hemangiomatosis: report of two cases and a pooled analysis

XIE Wan-mu ¹DAI Hua-ping ²JIN Mu-lan ¹WANG Zhen ²YANG Yuan-hua ³ZHAI Zhen-guo ¹WANG Chen²

作者信息

1. Department of Respiratory and Critical Care Medicine ,Beijing Chao-Yang Hospital,Capital Medical University,Beijing 100020,China
2. Beijing Key Laboratory of Respiratory and Pulmonary Circulation,Beijing Institute of Respiratory Medicine,Beijing 100020,China
3. Department of Pathology ,Beijing Chao-Yang Hospital,Capital Medical University,Beijing 100020,China
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摘要

Abstract

Background Pulmonary capillary hemangiomatosis (PCH) is a rare disease and no Chinese case has been reported yet.The disease is often misdiagnosed and its clinical characteristics are incompletely described.The aim of this study was to describe two Chinese cases and to clarify the clinical and radiographic parameters of patients with PCH.Methods Two PCH cases were presented and other cases were searched from the English literature.All available clinical and radiographic data were collected from 62 literature reported PCH cases.A pooled analysis of total 64 cases was made.Results Dyspnea and hemoptysis were the most common clinical symptoms of PCH.Pulmonary hypertension (PH)was found in 78％ of the reported cases.PCH typically showed characteristic diffuse or patchy ground-glass opacities (GGOs) and/or multiple ill-defined centrilobular nodules in the computed tomography.Conclusions The diagnosis of PCH requires a high clinical suspicion.However,both clinical presentations and radiographic studies often provide clues to the diagnosis,which may prompt early lung biopsy for a definite diagnosis.

关键词

pulmonary capillary hemangiomatosis/ pulmonary hypertension/ lung biopsy

Key words

pulmonary capillary hemangiomatosis/ pulmonary hypertension/ lung biopsy

引用本文复制引用

XIE Wan-mu,DAI Hua-ping,JIN Mu-lan,WANG Zhen,YANG Yuan-hua,ZHAI Zhen-guo,WANG Chen..Clinical features and imaging findings in pulmonary capillary hemangiomatosis: report of two cases and a pooled analysis[J].中华医学杂志（英文版）,2012,125(17):3069-3073,5.

基金项目

This work was supported by a grant from the Major International Joint Research Project of Natural Science Foundation of China (No.30810103904). （No.30810103904）

中华医学杂志（英文版）

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ISSN：0366-6999

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