中国全科医学2012,Vol.15Issue(32):3776-3778,3.DOI:10.3969/j.issn.1007-9572.2012.11.068
连枷臂综合征的临床特征分析
Clinical Analysis of Flail Arm Syndrome
王特 1孙新刚 1杨欢 1刘运海1
作者信息
- 1. 410008湖南省长沙市,中南大学湘雅医院神经内科
- 折叠
摘要
Abstract
Objective To study the clinical features of flail arm syndrome ( FAS ). Methods Clinical data of 8 cases of FAS admitted to the department of neurology in our hospital from June 1st 2010 to December 1st 2011 were retrospectively analyzed to summarize its clinical features. Results The 8 cases in the study were mainly characterized by muscle atrophy of proximal upper extremity, mostly in middle - aged people [ ( 48. 2±4. 8 ) years ] and males ( the ratio of male to female was 7 : 1 ). The initial symptoms were mainly weakness of bilateral upper extremities ( 62. 5% ), accompanied by fasciculation. EMG showed extensive neurogenic damage ( three or more than three segments ). Muscle biopsy showed 8 cases had muscle fiber atrophy, 7 cases had type grouping and 3 cases had target fibers. Conclusion FAS patients have a relatively slow progression of disease and longer survival time. It might be a clinical variant of typical amyotrophic lateral sclerosis and its morbidity might be related to genetic abnormality and race.关键词
连枷臂综合征/肌萎缩侧索硬化/运动神经元病Key words
Flail arm syndrome/ Amyotrophic lateral sclerosis/ Motor neuron disease分类
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王特,孙新刚,杨欢,刘运海..连枷臂综合征的临床特征分析[J].中国全科医学,2012,15(32):3776-3778,3.