临床神经病学杂志2013，Vol.26Issue(2)：144-146,3.
带状型灰质异位合并分离型脑裂畸形和透明隔部分缺如的临床和影像学特点(附1例报告)
Clinical and imaging features of subcortical band heterotopia complicated with open-lip schizencephaly and septum pellucidum partial deletion (report of 1 case)
杨中原 1任传成1
作者信息
- 1. 200240 复旦大学附属上海市第五人民医院神经内科
- 折叠
摘要
Abstract
Objective To explore the clinical and imaging features of subcortical band heterotopia ( SBH) complicated with open-lip schizencephaly ( OS) and septum pellucidum partial deletion ( SPPD). Methods The clinical data of one SBH patient complicated with OS and SPPD was analyzed retrospectively. Results The patient with juvenile onset, the right limb development in short, the spastic muscle tone of the right side, the motor dysfunction of the right side, and adolescent onset seizures, episodic disturbance of consciousness as the main symptoms. Cranial CT scan showed that left parietal schizencephaly with gray matter heterotopia. Cranial MRI scan showed that left parietal schizencephaly connected with the left ventricle; the schizencephaly was surrounded by a continuous tortuous-like low signal in T1WI and high signal in T2WI intensity (consistent with gray matter signal) ; the left ventricle expanded; part of the septum pellucidum dysplasia. Conclusions The manifestations of SBH patient complicated with OS and SPPD are epilepsy, mental retardation, growth retardation and nervous system dysfunction,etc. The imaging features are clear and regular gray matter appeared in the white matter between the lateral ventricles and gray matter, just like "double cortex" , besides OS and SPPD.关键词
灰质异位/脑裂畸形/临床特点/MRIKey words
gray matter heterotopia/schizencephaly/clinical feature/MRI分类
医药卫生引用本文复制引用
杨中原,任传成..带状型灰质异位合并分离型脑裂畸形和透明隔部分缺如的临床和影像学特点(附1例报告)[J].临床神经病学杂志,2013,26(2):144-146,3.
