青岛大学医学院学报2013，Vol.49Issue(4)：345-347,350,4.DOI:10.11712/qdyxy201304021
小儿孤立性心肌致密化不全13例临床分析
ISOLATED NON-COMPACTION CARDIOMYOPATHY IN CHILDREN: A CLINICAL ANALYSIS OF 13 CASES
郭玉秀 1聂娜娜 1司辉 1李荣 2李自普1
作者信息
- 1. 青岛大学医学院附属医院儿科,山东青岛 266003
- 2. 青岛大学医学院附属医院超声科,山东青岛 266003
- 折叠
摘要
Abstract
Objective To investigate the clinical characteristics of isolated non-compaction cardiomyopathy (NCCM) in children.Methods Clinical data of 13 NCCM children were analyzed retrospectively.Results There was no manifestations of embolism presented in all the 13 NCCM children,but eight of them had obvious cardiac dysfunction,12 had cardiac arrhythmia,of whom,four had premature ventricular beats.Typical echocardiographic changes were observed in all the 13 children,of whom,12were involved in the left ventricle alone,both ventricles involved in one; left ventricular enlargement was seen in nine,eight with decreased left ventricular ejection fraction,and nine had an increased pulmonary artery systolic pressure.During 0.5-4.4-year follow up,sudden death was noted in one case,two died of intractable heart failure; and three repeated hospitalization due to heart failure.Conclusion Cardiac dysfunction and arrhythmia are frequently observed in children with NCCM,and embolism is rare.Ultrasound cardiography is of great value in the diagnosis of NCCM——a disease of poor prognosis.关键词
孤立性心肌致密化不全/疾病特征/儿童Key words
isolated non-compaction cardiomyopathy/ disease attributes/ child分类
医药卫生引用本文复制引用
郭玉秀,聂娜娜,司辉,李荣,李自普..小儿孤立性心肌致密化不全13例临床分析[J].青岛大学医学院学报,2013,49(4):345-347,350,4.
