南方医科大学学报Issue(1)：1-4,4.
肝脏非特异性血管周上皮样细胞肿瘤：附1例报告
Hepatic perivascular epithelioid cell tumors- not otherwise specified:a case report
张晓刚 1王林 1蒋依娜 2万真 1李文智 1姚春和 1耿智敏 1吕毅1
作者信息
- 1. 西安交通大学医学院第一附属医院肝胆外科，陕西 西安 710061
- 2. 西安交通大学医学院第一附属医院病理科，陕西 西安 710061
- 折叠
摘要
Abstract
Neoplasms of perivascular epithelioid cells (PEComas) are characterized by epithelioid to spindle cells with eosinophilic to clear cytoplasm, an intimate relationship with blood vessels, and coexpression of myoid and melanocytic immunohistochemical markers. While most reported hepatic PEComas, such as angiomyolipoma (AML), behave in a benign fashion, emerging PEComas cases without typical characteristics require further clarification. We report a case of primary hepatic perivascular epithelioid cell tumors-not otherwise specified (HPEComas-NOS) with untypical pathological and immunohistochemical features compared to those of the benign hepatic AML cases. HPEComas-NOS may represent a special type of PEComas classified as having "malignant potential" or at "high risk of aggressive behavior", suggesting the need for further clarification of hepatic PEComas and long-term follow-up of patients with HPEComas-NOS.关键词
血管平滑肌脂肪瘤/肝脏非特异性血管周上皮样细胞肿瘤/血管周上皮样细胞肿瘤Key words
angiomyolipoma/hepatic perivascular epithelioid cell tumors-not otherwise specified/perivascular epithelioid cell tumors引用本文复制引用
张晓刚,王林,蒋依娜,万真,李文智,姚春和,耿智敏,吕毅..肝脏非特异性血管周上皮样细胞肿瘤：附1例报告[J].南方医科大学学报,2014,(1):1-4,4.
