中国卒中杂志Issue(7)：527-532,6.
儿童出血型烟雾病的损伤模式
Lesion Patterns of Hemorrhagic Type of Moyamoya Disease in Children
摘要
Abstract
Objective To analyze the lesion patterns of hemorrhagic type of moyamoya disease in children. <br> Methods The clinical and imaging data of 26 hemorrhagic type patients among 450 pediatric patients with moyamoya disease from December 2002 to December 2011 were analyzed retrospectively. According the location of hemorrhage, moyamoya disease patients were classified into three types, thalamic in 2 patients, non-thalamic parenchymal (basal ganglia and cerebral lobe) in 3 patients, primary ventricular hemorrhage in 21 patients. All patients received digital silhouette angiography (DSA). The ipsilateral anterior choroidal artery and posterior communicating artery (AChA-PComA) were evaluated by the modified Morioka's 3-points grading system. The distribution of lesion patterns and the relationship with AChA-PComA and posterior choroidal artery (PChA) were analyzed. <br> Results All the patients suffered one episode of bleeding. A total of 4 patients complicated with aneurysms, 1 was located in the anterior cerebral artery, 1 in the anterior choroidal artery, 2 in the PChA. In the stage of normal or mild dilation, the non-thalamic parenchymal type was the most frequent type (2/3, 66.7%), the PChA were all in stage 1;in the stage of severe dilation with abnormal extension, intraventricular hemorrhage was most common (16/17, 94.1%), the PChA were all in stage 1;in the stage of non-visualization, intraventricular hemorrhage was still the most common type (4/6, 66.7%), others were found in thalamus (2/6, 33.3%). The PChA all manifested dilation and branch extension (P<0.05). <br> Conclusion Intraventricular hemorrhage was the most common type in pediatric hemorrhagic moyamoya patients; compared with other lesion patterns, the dilation and branch extension of AChA-PComA accounted for a large proportion;in the stage of non-visualization of AChA-PComA, PChA all showed dilation and branch extension.关键词
儿童/烟雾病/脑出血/血管造影术Key words
Children/Moyamoya disease/Hemorrhage/Cerebral angiography引用本文复制引用
刘鹏,暴向阳,韩聪,李德生,咸鹏,杨伟中,宗睿,张正善,段炼..儿童出血型烟雾病的损伤模式[J].中国卒中杂志,2013,(7):527-532,6.基金项目
国家自然科学基金资助项目（81171083）@@@@首都临床特色应用研究（Z121107001012058）@@@@中国人民解放军第307医院创新科研基金重点项目 （）
