中国实用内科杂志2017，Vol.37Issue(6)：484-487,4.DOI:10.19538/j.nk2017060103
干燥综合征的肺部病变
Pulmonary involvement in Sj(o)gren's syndrome
李霞 1费允云 2张垣2
作者信息
- 1. 首都医科大学宣武医院风湿免疫科
- 2. 北京协和医院北京协和医院风湿免疫科
- 折叠
摘要
Abstract
Extraglandular organ systems of Sj(o)gren's syndrome (SS)may frequently be involved,including the respiratory system.Pulmonary involvement is defined by respiratory symptoms,pulmonary function or radiographic abnormalities.Clinical manifestations vary.Bronchiolitis and bronchiectasis are the most common airway manifestations.Interstitial lung disease is the most common lung disease of SS.Patients with SS are at high risk of lung lymphoma.Other lung abnormalities include pulmonary artery hypertension (PAH),pulmonary cystic lesions,amyloidosis,and pleural disease.Corticosteroids alone or in combination with other immunosuppressors are quite necessary for the patients with progressive chest symptoms.PAH targeted therapy is recommended in SS-PAH patients.关键词
干燥综合征/气道病变/间质性肺病/肺动脉高压Key words
Sj(o)gren syndrome/airway disease/interstitial lung disease/pulmonary artery hypertension分类
医药卫生引用本文复制引用
李霞,费允云,张垣..干燥综合征的肺部病变[J].中国实用内科杂志,2017,37(6):484-487,4.
