婴儿血管瘤合并先天性门体静脉分流1例OA
A case of infantile hemangioma with congenital portosystemic shunt
报告1例婴儿血管瘤合并先天性门体静脉分流.患儿男,2个月7天,因全身皮肤散在红色肿物及黄染2个月余,加重1周就诊.皮肤科检查:全身散在分布约54块大小不等红色、暗红色斑块,质软,界限清楚.腹部彩超示肝右叶见1 cm ×0.8 cm高回声结节,脾大、脾脏不均质回声结节,肝中静脉与门静脉矢状部多发交通支,其内可见花色血流信号.上腹部CT示肝脏多发不规则低密度影,增强扫描病灶明显强化,其内可见粗大血管.诊断:①婴儿血管瘤;②先天性门体静脉分流(合并动静脉瘘);③巨细胞病毒病.予普萘洛尔口服治疗后,患儿皮肤血管瘤基本消退,CPSS分支闭合,随访1年患儿生长发育同正常同龄儿.
A case of infantile hemangioma complicated with congenital portosystemic shunt is reported.A 2-month and 7-day-old boy presented with scattered red skin lesions and yellowish skin for over 2 months,and aggravated for 1 week.The dermatology examination revealed about 54 scattered red and dark red plaques of various sizes with a soft texture and clear boundaries.Ab-dominal ultrasound showed hyperechoic nodules(1 cm × 0.8 cm)in the right lobe of the liver and enlarged spleen with heterogeneous echogenic nodules,along with multiple vascular branches be-tween the middle hepatic vein and the sagittal portal vein,in which blue blood flow signal was vis-ible.CT of the upper abdomen showed multiple irregular low-density shadows in the liver,and the lesions were significantly enhanced on the enhancement scan,and large blood vessels were visible in the lesions.Diagnosis:Infantile hemangioma;Congenital portosystemic shunt complicated with arteriovenous fistula;Cytomegalovirus disease.After treatment with oral propranolol,the cutane-ous hemangioma almost completely subsided and the CPSS branches were closed.The child grew and developed normally during a 1-year follow-up.
杨星星;罗丹;刘凯林;马岩;梁丽俊
宁夏医科大学,宁夏 银川 750004||宁夏医科大学总医院,宁夏 银川 750000宁夏医科大学,宁夏 银川 750004||宁夏医科大学总医院,宁夏 银川 750000西北大学附属医院西安市第三医院,陕西 西安 710018宁夏医科大学,宁夏 银川 750004||宁夏医科大学总医院,宁夏 银川 750000宁夏医科大学,宁夏 银川 750004||宁夏医科大学总医院,宁夏 银川 750000
婴儿血管瘤先天性门体静脉分流普萘洛尔超声检查
infantile hemangiomascongenital portosystemic shuntspropranololultra-sound
《皮肤性病诊疗学杂志》 2024 (1)
36-40,5
宁夏自然科学基金(2023AAC03631)
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