Abstract
Objective To investigate the development of auditory performance in children with Mondini malformation aged 0-3 years within 5 years after cochlear implantation(CI).Methods A retrospective cohort study design was used in this study,and a total of 235 children who underwent unilateral CI surgery within 36 months of age were included.Based on the imaging findings,they were divided into Mondini group(47 cases)and control group with normal inner ear structure(188 cases).Auditory performance was assessed by the same group of uniformly standardized trained professionals using the Categories of auditory performance(CAP)scale.The assessment was performed before CI and at 1,2,3,6,9,12,18,24,30,36,42,48,54,and 60 months after switch-on,respectively.Results The CAP scores of the two groups were significantly different at pre-CI and at 1 month after switch on(P<0.05),and there were no significant differences at the rest of the follow-up time points(P>0.05).At 42 months,48 months,54 months,and 60 months after start-up,the CAP scores of the children in both groups were close to 7.There was a significant difference between the preoperative CAP scores and the CAP scores at 1,2,3,6,9,12,18,24,30,36,42,48,54,and 60 months after start-up in the Mondini group(P<0.05).Within 1 year of switch-on,significant differences were found between 1 month after switch-on and 3 months after switch-on,2 months after switch-on and 3 months after switch-on,3 months after switch-on and 9 months after switch-on,6 months after switch-on and 9 months after switch-on,and 9 months after switch-on and 18 months after switch-on(P<0.05);whereas between 1 year and 3 years after switch-on,12 months after switch-on and 24 months after switch-on,18 months after switch-on and 24 months after switch-on,24 months after switch-on and 36 months after switch-on,30 months after switch-on and 42 months after switch-on were significantly different(P<0.05);and there were no differences between the follow-up time points after 3 years of switch-on(P>0.05).Conclusion Cochlear implantation is an effective way to improve auditory performance in children with Mondini malformation.Children with Mondini malformation aged 0-3 years can obtain a significant improvement in auditory performance within 3 years after CI and enter a plateau period after 3 years.The benefit of CI in children with Mondini malformation is comparable to that in children with normal inner ear structure.关键词
Mondini畸形/人工耳蜗植入/听觉能力分级Key words
Mondini deformity/Cochlear implantation/Categories of auditory performance分类
医药卫生
