临床小儿外科杂志2024，Vol.23Issue(8)：706-710,5.DOI:10.3760/cma.j.cn101785-202406012-002
重视胆道闭锁肝门空肠吻合术后长期存活患儿肺血管并发症
Emphasis on pulmonary vascular complications in children with a long-term survival after hepatoportal jejunostomy for biliary atresia
摘要
Abstract
In children with a long-term survival after hepato-jejunostomy for biliary atresia(BA),chro-nic liver cirrhosis leads to hepatopulmonary syndrome(HPS)and portopulmonary hypertension(PoPH),cau-sing diverse respiratory and circulatory system symptoms.The incidence of such complications in BA children is higher than that of other chronic liver diseases.With a faster progression,it endangers life in some severe cases.HPS and PoPH may coexist in the same child.Improving the understanding of HPS/PoPH,making an early di-agnosis,rational selection of medication and proper timing of liver transplantation require multidisciplinary col-laborations.关键词
胆道闭锁/外科手术/手术后并发症/肝肺综合征/肺动脉高压Key words
Biliary Atresia/Surgical Procedures,Operative/Postoperative Complications/Hepatopul-monary Syndrome/Pulmonary Arterial Hypertension引用本文复制引用
陈功,张杰..重视胆道闭锁肝门空肠吻合术后长期存活患儿肺血管并发症[J].临床小儿外科杂志,2024,23(8):706-710,5.基金项目
上海市自然科学基金(19ZR1406600) Shanghai Municipal Natural Science Foundation(19ZR1406600) （19ZR1406600）
