一致性心室动脉连接合并平行动脉干系列畸形超声心动图特征的病例系列报告OA北大核心

Background Hearts with concordant ventriculoarterial connections but parallel arterial trunks are very rare.Echocardiography is one of the important methods for diagnosis.Objective To explore the echocardiographic diagnostic features of S.D.L-type anatomically corrected malposition of the great arteries(ACMGA)and isolated ventricular inversion(IVI),characterized by concordant ventriculoarterial connections but parallel arterial trunks.Design Case series report.Methods A retrospective collection of consecutive cases diagnosed with ACMGA and IVI at Beijing Anzhen Hospital from June 2008 to March 2025.The clinical baseline data,imaging results,treatment,and follow-up of the patients were extracted from the hospital's medical record system,and the echocardiographic features and diagnostic criteria were summarized.Main outcome measures Echocardiographic features and clinical treatments.Results Among 13 patients,10 cases were S.D.L-type ACMGA with concordant atrioventricular connections,and 3 cases were IVI with discordant atrioventricular connections.Nine cases underwent surgical treatment(7 radical and 2 palliative).Three cases were complicated with major anomalies,and 1 case had minor anomalies.Echocardiographic common features included:a.Both the aorta and pulmonary artery originated from the corresponding ventricle and were arranged in parallel.b.This malformation was usually associated with a ventricular septal defect(VSD),bilateral atrial appendage juxtaposition,pulmonary stenosis,and other intracardiac anomalies.In S.D.L-type ACMGA:a.Atrioventricular connection was concordant.b.The aorta was located to the left of the pulmonary artery.c.The conal muscle was present between the two arteries,mostly beneath the aorta,with no fibrous continuity between the aortic and mitral valves.d.The left ventricular outflow tract was elongated.e.Treatment was directed at associated anomalies.In IVI:a.Atrioventricular connection was discordant.b.The aorta was located to the right of the pulmonary artery.c.Fibrous continuity was preserved.d.Surgical treatment required an atrial baffle procedure combined with radical correction of associated anomalies.Conclusion The Van Praagh segmental analysis principle aids in diagnosing malformations with concordant ventriculoarterial connections and parallel arterial trunks.Accurate preoperative echocardiographic diagnosis is crucial for surgical planning.